What are the characteristic clinical ocular findingsin this patient?

Answer
Pulsatile exophthalmos due to transmission of the cerebrospinal fluid (CSF) wave.
Other findings include:
Lisch's nodule
Plexiform neuroma of the eyelid.
Ectopia uvea

What extra-ocular features may be present?

Answer
Cafe-au-lait spot
Neurofibroma
Axillary freckles
Hypertension due to phaeochromocytoma.