Which stain had been used? Answer Congo red. a What is the diagnosis? a Answer Lattice dystrophy. The corneal stroma shows the presence of discrete substances which are stained red with Congo red What do you know of Meretoja's syndrome? a Answer It is also called type IV familial amyloid polyneuropathy of the Finnish type. Systemic amyloid deposition is the feature. The lattice dystrophy in this disorder is classed as type II. The lattice lines typically extend to the limbus. Compared with type I lattice dystrophy (the commonest), recurrent erosion and visual disturbance are uncommon. The systemic amyloid deposition causes mask like facies and cranial nerve palsies. Involvement of the facial nerves causes bilateral facial weakness.
Which stain is used and what is the main abnormality seen? a Answer Alcian blue. The corneal stroma shows diffused deposition of bluish materials. The diagnosis is macular dystrophy. What systemic conditions may be associated with this condition? Name three. a Answer Macular dystrophy occurs in a group of conditions collectively known as mucopolysaccharidoses. They are caused by a specific enzyme defect. Conditions within this group that have cornea involvement include: Hurler's syndrome, Scheie's syndrome and Morquio's syndrome.
